We do the sorting. You do the medicine.
Cardiac06 / 22

Unrepaired VSD for adenotonsillectomy4-year-old boy, 13 kg, for elective adenotonsillectomy

From memory: the diagnosis and the notes are hidden. Answer each question aloud, then press Show.

Know this first

  • A Qp:Qs over 1.5:1 means pulmonary blood flow must be managed.
  • Air in any IV line can cross a shunt to the systemic side.
  • Endocarditis prophylaxis is for the highest-risk groups, not an unrepaired acyanotic VSD.
  • Laryngospasm: CPAP and propofol, then suxamethonium 1–2 mg/kg IV or 4–5 mg/kg IM.

The patient

4-year-old boy, 13 kg, for elective adenotonsillectomy; loud snoring with witnessed apnoeas. Unrepaired moderate perimembranous VSD, left-to-right, Qp:Qs 1.8:1; weight below the 5th centile. No regular drugs; no pulmonary hypertension on last echo. Vitals: HR 118, BP 94/52, SpO2 98% on air, RR 26.

The examiner asks

Answer aloud, then press Show.

  1. Consider

    What are the issues?

    Show the answerHide the answer
    • A 4-year-old with an unrepaired moderate VSD and apnoeas, for adenotonsillectomy. Patient
    • As a young child his output depends on heart rate, so bradycardia is poorly tolerated.
    • His shunt is left-to-right at 1.8:1, so I limit extra pulmonary flow. Disease
    • His poor growth makes me ask about sweating, fast breathing, poor feeding and chest infections.
    • Witnessed apnoeas mean obstructive sleep apnoea, with obstruction and desaturation after surgery. Surgery
  2. Prepare

    How will you prepare?

    Show the answerHide the answer
    • Recent echo for his shunt size, direction and pulmonary pressure. Disease
    • No endocarditis prophylaxis: his unrepaired acyanotic VSD isn't a highest-risk lesion.
    • Every IV line and syringe de-aired before it reaches him.
    • Oral midazolam 0.2–0.5 mg/kg so he arrives settled. Patient
    • Overnight stay with oximetry until he holds his saturation on air while asleep. After surgery
  3. Plan

    How do you conduct the anaesthetic?

    Show the answerHide the answer
    • Gas induction with sevoflurane, then IV access; his shunt barely changes the speed. Disease
    • No high oxygen or hyperventilation, which lower PVR and increase his shunt.
    • Avoid sharp rises in systemic resistance from light anaesthesia or pain.
    • Suction blood from his pharynx before extubation; blood triggers laryngospasm. Airway
    • Dexamethasone 0.15 mg/kg, ondansetron 50–100 mcg/kg, paracetamol 15 mg/kg IV. After surgery
    • OSA makes him opioid-sensitive, so I halve his opioid doses. Disease
  4. Crisis

    At extubation he develops laryngospasm; SpO2 falls to 70% and HR to 58. What do you do?

    Show the answerHide the answer
    • Laryngospasm with hypoxic bradycardia, HR 58: PALS bradycardia, and airway first. (Crisis)
    • Call for help; tight mask, 100% oxygen, CPAP 15–20 cmH2O, firm jaw thrust.
    • SpO2 70% already: suxamethonium 1–2 mg/kg IV, or 4–5 mg/kg IM.
    • His slow rate is hypoxic, so oxygen is the treatment; atropine 0.02 mg/kg goes with the suxamethonium.
    • Hypoxia also raises his PVR and can reverse flow across his VSD.
    • HR still under 60 and poorly perfused despite good ventilation: start CPR.
    • Bradycardia persisting once oxygenated: adrenaline 0.01 mg/kg IV.

Fatal mistakes

  • Air in his IV lines.
  • Slow, stepwise hesitation in treating laryngospasm.
  • No drug plan for hypoxic bradycardia.
  • Sending him home the same day.

Checked against: Stoelting 8e · Barash 9e · AHA and AAP guidelines: pediatric advanced life support (2025)

Report a problem with this case

Mark Got it only if you said every point. Again brings the case back tomorrow; Got it brings it back in 3, then 7, 14 and 30 days.

All Cardiac casesBack to today